Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis

Disease • C2717865

Definition

Group of systemic vasculitis with a strong association with ANCA. The disorders are characterized by necrotizing inflammation of small and medium size vessels, with little or no immune-complex deposits in vessel walls.

Synonyms

Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis • Anti Neutrophil Cytoplasmic Antibody Associated Vasculitis • ANCA-Associated Vasculitide • Vasculitide, ANCA-Associated • Pauci-Immune Vasculitis • Pauci Immune Vasculitis • Pauci-Immune Vasculitides • Vasculitides, Pauci-Immune • Vasculitis, Pauci-Immune • ANCA-Associated Vasculitides • ANCA Associated Vasculitides • ANCA Associated Vasculitis • ANCA-Associated Vasculitis • Vasculitis, ANCA-Associated • Vasculitides, ANCA-Associated • Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis [Disease/Finding]

Linked items?Related concepts, ordered by their global importance in the network.

Autoimmune Diseases    Systemic Vasculitis    Churg-Strauss Syndrome    Wegener Granulomatosis   

Related concepts

# Concept name Type Relation Support Score
1 Systemic Vasculitis Disease Known Explain 249.22076
2 Wegener Granulomatosis Disease Known Explain 209.05422
3 Churg-Strauss Syndrome Disease Known Explain 179.02409
4 Autoimmune Diseases Disease Known Explain 38.49169
5 Rheumatoid Vasculitis Disease Inferred Explain 32.49654
6 Polyarteritis Nodosa Disease Inferred Explain 26.44433
7 FCGR3B gene Gene Inferred Explain 19.34635
8 Lung Diseases, Interstitial Disease Inferred Explain 15.51057
9 Adrenal Cortex Hormones Compound Inferred Explain 11.86701
10 Vasculitis Disease Inferred Explain 10.97100
11 Granuloma Disease Inferred Explain 8.14333
12 Arteritis Disease Inferred Explain 4.55959
13 zafirlukast Compound Inferred Explain 3.81759
14 Skin Diseases, Vascular Disease Inferred Explain 2.84738
15 Rheumatoid Arthritis Disease Inferred Explain 1.62106
16 Anti-Glomerular Basement Membrane Disease Disease Inferred Explain 0.38015
17 Vasculitis, Central Nervous System Disease Inferred Explain 0.36008
18 VASCULITIS, LYMPHOCYTIC, CUTANEOUS SMALL VESSEL Disease Inferred Explain 0.29156
19 VASCULITIS, LYMPHOCYTIC, NODULAR Disease Inferred Explain 0.29156
20 Giant Cell Arteritis Disease Inferred Explain 0.25650
21 Malignant Atrophic Papulosis Disease Inferred Explain 0.25048
22 Mucocutaneous Lymph Node Syndrome Disease Inferred Explain 0.21590
23 Histiocytosis, Langerhans-Cell Disease Inferred Explain 0.18854
24 Hypersensitivity vasculitis Disease Inferred Explain 0.18747
25 Aortitis Disease Inferred Explain 0.17076
26 Shwartzman Phenomenon Disease Inferred Explain 0.17069
27 Retinal Vasculitis Disease Inferred Explain 0.16830
28 Thromboangiitis Obliterans Disease Inferred Explain 0.16687
29 Vasculitis Adverse Event Disease Inferred Explain 0.16678
30 Takayasu Arteritis Disease Inferred Explain 0.16678
31 AIDS Arteritis, Central Nervous System Disease Inferred Explain 0.16147
32 Phlebitis Disease Inferred Explain 0.15943
33 Henoch-Schoenlein Purpura Disease Inferred Explain 0.15913
34 Behcet Syndrome Disease Inferred Explain 0.15668
35 Sarcoidosis, Pulmonary Disease Inferred Explain 0.14917
36 Eosinophilic Granuloma Disease Inferred Explain 0.14417
37 Extrinsic allergic alveolitis Disease Inferred Explain 0.14241
38 Lymphocyte Other Inferred Explain 0.13636
39 Idiopathic Interstitial Pneumonias Disease Inferred Explain 0.13152
40 Desquamative interstitial pneumonia Disease Inferred Explain 0.12247
41 Radiation Pneumonitis Other Inferred Explain 0.12215
42 Glomerulonephritis Disease Inferred Explain 0.11726
43 Pneumoconiosis Disease Inferred Explain 0.11052
44 SURFACTANT METABOLISM DYSFUNCTION, PULMONARY, 1 Disease Inferred Explain 0.09680
45 Membranous glomerulonephritis Disease Inferred Explain 0.09494
46 Oculovestibuloauditory syndrome Disease Inferred Explain 0.09194
47 AUTOIMMUNE DISEASE, SUSCEPTIBILITY TO, 1 Disease Inferred Explain 0.08756
48 Antiphospholipid Syndrome Disease Inferred Explain 0.08600
49 Hepatitis, Autoimmune Disease Inferred Explain 0.08494
50 Granuloma Annulare Disease Inferred Explain 0.08493
51 Immune Complex Diseases Disease Inferred Explain 0.08196
52 Arterial Occlusive Diseases Disease Inferred Explain 0.07890
53 Autoimmune Diseases of the Nervous System Disease Inferred Explain 0.07666
54 Ophthalmia, Sympathetic Disease Inferred Explain 0.07658
55 Granuloma, Foreign-Body Disease Inferred Explain 0.07615
56 Pyogenic granuloma Disease Inferred Explain 0.07590
57 Dermatitis Herpetiformis Disease Inferred Explain 0.07552
58 Vascular Diseases Disease Inferred Explain 0.07522
59 Epithelioid hemangioma of skin Disease Inferred Explain 0.07435
60 Autoimmune hemolytic anemia Disease Inferred Explain 0.07239
61 Pemphigus Disease Inferred Explain 0.06992
62 Heparin Compound Inferred Explain 0.06871
63 Bullous pemphigoid Disease Inferred Explain 0.06508
64 Granuloma, Respiratory Tract Disease Inferred Explain 0.06387
65 Polyendocrinopathies, Autoimmune Disease Inferred Explain 0.06147
66 Aortic Diseases Disease Inferred Explain 0.06120
67 Giant Cell Granuloma Disease Inferred Explain 0.06027
68 Autoimmune Lymphoproliferative Syndrome Disease Inferred Explain 0.05913
69 Vascular Hemostatic Disorders Disease Inferred Explain 0.05709
70 Purpura, Thrombocytopenic, Idiopathic Disease Inferred Explain 0.05687
71 Beryllium Compound Inferred Explain 0.05434
72 IGA Glomerulonephritis Disease Inferred Explain 0.05159
73 Lambert-Eaton Myasthenic Syndrome Disease Inferred Explain 0.04765
74 Addison Disease Disease Inferred Explain 0.04655
75 Autoimmune thyroiditis Disease Inferred Explain 0.04649
76 Graves Disease Disease Inferred Explain 0.04400
77 Warfarin Compound Inferred Explain 0.04322
78 Lupus Nephritis Disease Inferred Explain 0.04228
79 Hydroxycorticosteroids Compound Inferred Explain 0.04060
80 Livedo Reticularis Disease Inferred Explain 0.03545
81 Immune System Diseases Disease Inferred Explain 0.03310
82 Sarcoidosis Disease Inferred Explain 0.03241
83 Sneddon Syndrome Disease Inferred Explain 0.03109
84 17-Ketosteroids Compound Inferred Explain 0.03099
85 Skin Diseases, Vesiculobullous Disease Inferred Explain 0.02902
86 Glucocorticoids Compound Inferred Explain 0.02748
87 Lymphoproliferative Disorders Disease Inferred Explain 0.02487
88 SERPINA1 gene Gene Inferred Explain 0.02428
89 Lung Injury Other Inferred Explain 0.02409
90 Cholecalciferol Compound Inferred Explain 0.02407
91 Lupus Erythematosus, Systemic Disease Inferred Explain 0.02403
92 Foreign-Body Reaction Disease Inferred Explain 0.02382
93 Aortic Arch Syndromes Disease Inferred Explain 0.02380
94 Lupus Vasculitis, Central Nervous System Disease Inferred Explain 0.02328
95 Thrombophlebitis Disease Inferred Explain 0.02276
96 Panuveitis Disease Inferred Explain 0.02221
97 Eosinophilia Disease Inferred Explain 0.02209
98 Peripheral Vascular Diseases Disease Inferred Explain 0.02169
99 Lung diseases Disease Inferred Explain 0.02169
100 sulforafan Compound Inferred Explain 0.02169