|
#
|
Entity
|
Type
|
Relation
|
Support
|
Relative specificity
|
|
1
|
Lipoylprotein
|
Compound
|
Known
|
Explain
|
|
|
2
|
Dihydrolipoylprotein
|
Compound
|
Known
|
Explain
|
|
|
3
|
lipoamide binding
|
Function
|
Known
|
Explain
|
|
|
4
|
Protein N6-(lipoyl)lysine
|
Compound
|
Known
|
Explain
|
|
|
5
|
Enzyme N6-(dihydrolipoyl)lysine
|
Compound
|
Known
|
Explain
|
|
|
6
|
Glutaryl-CoA
|
Compound
|
Known
|
Explain
|
|
|
7
|
2-Oxoadipate
|
Compound
|
Known
|
Explain
|
|
|
8
|
dihydrolipoamide dehydrogenase activity
|
Function
|
Known
|
Explain
|
|
|
9
|
lipoate metabolic process
|
Function
|
Known
|
Explain
|
|
|
10
|
dihydrolipoamide metabolic process
|
Function
|
Known
|
Explain
|
|
|
11
|
Enzyme N6-(lipoyl)lysine
|
Compound
|
Known
|
Explain
|
|
|
12
|
acrosomal matrix
|
Component
|
Known
|
Explain
|
|
|
13
|
5,10-methylenetetrahydrofolate
|
Compound
|
Known
|
Explain
|
|
|
14
|
PDHX gene
|
Gene
|
Known
|
Explain
|
|
|
15
|
oxoglutarate dehydrogenase complex
|
Component
|
Known
|
Explain
|
|
|
16
|
OGDH gene
|
Gene
|
Known
|
Explain
|
|
|
17
|
Maple Syrup Urine Disease
|
Disease
|
Known
|
Explain
|
|
|
18
|
succinyl-coenzyme A
|
Compound
|
Known
|
Explain
|
|
|
19
|
regulation of acetyl-CoA biosynthetic process from pyruvate
|
Function
|
Known
|
Explain
|
|
|
20
|
pyruvate dehydrogenase complex location
|
Component
|
Known
|
Explain
|
|
|
21
|
Sperm Capacitation
|
Function
|
Known
|
Explain
|
|
|
22
|
5,6,7,8-tetrahydrofolic acid
|
Compound
|
Known
|
Explain
|
|
|
23
|
lysine catabolism
|
Function
|
Known
|
Explain
|
|
|
24
|
Gastrulation
|
Function
|
Known
|
Explain
|
|
|
25
|
Leigh Disease
|
Disease
|
Known
|
Explain
|
|
|
26
|
Glycine
|
Compound
|
Known
|
Explain
|
|
|
27
|
Pyruvic Acid
|
Compound
|
Known
|
Explain
|
|
|
28
|
alpha-ketoglutarate
|
Compound
|
Known
|
Explain
|
|
|
29
|
Citrate Cycle (TCA Cycle) Pathway
|
Function
|
Known
|
Explain
|
|
|
30
|
branched chain family amino acid catabolic process
|
Function
|
Known
|
Explain
|
|
|
31
|
2-oxoglutarate metabolic process
|
Function
|
Known
|
Explain
|
|
|
32
|
regulation of membrane potential
|
Function
|
Known
|
Explain
|
|
|
33
|
mitochondrial electron transport, NADH to ubiquinone
|
Function
|
Known
|
Explain
|
|
|
34
|
Glycine, Serine and Threonine Metabolism Pathway
|
Function
|
Known
|
Explain
|
|
|
35
|
Valine, Leucine and Isoleucine Degradation Pathway
|
Function
|
Known
|
Explain
|
|
|
36
|
Acetyl Coenzyme A
|
Compound
|
Known
|
Explain
|
|
|
37
|
Ammonia
|
Compound
|
Known
|
Explain
|
|
|
38
|
Pyruvate Metabolism Pathway
|
Function
|
Known
|
Explain
|
|
|
39
|
Flagella
|
Component
|
Known
|
Explain
|
|
|
40
|
Glycolysis/Gluconeogenesis Pathway
|
Function
|
Known
|
Explain
|
|
|
41
|
Citric Acid Cycle
|
Function
|
Known
|
Explain
|
|
|
42
|
DLST gene
|
Gene
|
Inferred
|
Explain
|
|
|
43
|
Carbon Dioxide
|
Compound
|
Known
|
Explain
|
|
|
44
|
SLC2A4 gene
|
Gene
|
Known
|
Explain
|
|
|
45
|
PSMD4 gene
|
Gene
|
Known
|
Explain
|
|
|
46
|
lipoic acid binding
|
Function
|
Inferred
|
Explain
|
|
|
47
|
Coenzyme A
|
Compound
|
Known
|
Explain
|
|
|
48
|
cell redox homeostasis
|
Function
|
Known
|
Explain
|
|
|
49
|
NAD or NADH binding
|
Function
|
Known
|
Explain
|
|
|
50
|
NADH
|
Compound
|
Known
|
Explain
|
|
|
51
|
Aging
|
Function
|
Known
|
Explain
|
|
|
52
|
AMT gene
|
Gene
|
Inferred
|
Explain
|
|
|
53
|
Nicotinamide adenine dinucleotide (NAD)
|
Compound
|
Known
|
Explain
|
|
|
54
|
Mitochondrial matrix
|
Component
|
Known
|
Explain
|
|
|
55
|
GLDC gene
|
Gene
|
Inferred
|
Explain
|
|
|
56
|
OGDHL gene
|
Gene
|
Inferred
|
Explain
|
|
|
57
|
FAD binding
|
Function
|
Known
|
Explain
|
|
|
58
|
cellular nitrogen compound metabolic process
|
Function
|
Known
|
Explain
|
|
|
59
|
Protons
|
Compound
|
Known
|
Explain
|
|
|
60
|
DLAT gene
|
Gene
|
Inferred
|
Explain
|
|
|
61
|
PDHB gene
|
Gene
|
Inferred
|
Explain
|
|
|
62
|
LIAS gene
|
Gene
|
Inferred
|
Explain
|
|
|
63
|
Dihydrolipoamide dehydrogenase
|
Domain
|
Inferred
|
Explain
|
|
|
64
|
lipoate biosynthetic process
|
Function
|
Inferred
|
Explain
|
|
|
65
|
RB1CC1 gene
|
Gene
|
Known
|
Explain
|
|
|
66
|
electron carrier activity
|
Function
|
Known
|
Explain
|
|
|
67
|
MAP1LC3A gene
|
Gene
|
Known
|
Explain
|
|
|
68
|
ULK2 gene
|
Gene
|
Known
|
Explain
|
|
|
69
|
lipoic acid metabolic process
|
Function
|
Inferred
|
Explain
|
|
|
70
|
DBT gene
|
Gene
|
Inferred
|
Explain
|
|
|
71
|
GABARAPL1 gene
|
Gene
|
Known
|
Explain
|
|
|
72
|
oxidoreductase activity, acting on sulfur group of donors, NAD or NADP as acceptor
|
Function
|
Inferred
|
Explain
|
|
|
73
|
resveratrol
|
Compound
|
Known
|
Explain
|
|
|
74
|
PDHA1 gene
|
Gene
|
Inferred
|
Explain
|
|
|
75
|
oxidoreductase activity
|
Function
|
Known
|
Explain
|
|
|
76
|
Mitochondria
|
Component
|
Known
|
Explain
|
|
|
77
|
AADAT gene
|
Gene
|
Inferred
|
Explain
|
|
|
78
|
cellular amide metabolic process
|
Function
|
Inferred
|
Explain
|
|
|
79
|
BCKDHB gene
|
Gene
|
Inferred
|
Explain
|
|
|
80
|
PDHA2 gene
|
Gene
|
Inferred
|
Explain
|
|
|
81
|
GRB2 gene
|
Gene
|
Known
|
Explain
|
|
|
82
|
BCKDHA gene
|
Gene
|
Inferred
|
Explain
|
|
|
83
|
GCDH gene
|
Gene
|
Inferred
|
Explain
|
|
|
84
|
CYLC1 gene
|
Gene
|
Inferred
|
Explain
|
|
|
85
|
Proteolysis
|
Function
|
Known
|
Explain
|
|
|
86
|
Oxidation-Reduction
|
Function
|
Known
|
Explain
|
|
|
87
|
cofactor metabolic process
|
Function
|
Inferred
|
Explain
|
|
|
88
|
mitochondrial oxoglutarate dehydrogenase complex
|
Component
|
Inferred
|
Explain
|
|
|
89
|
cytosolic oxoglutarate dehydrogenase complex
|
Component
|
Inferred
|
Explain
|
|
|
90
|
Dihydrolipoamide succinyltransferase
|
Domain
|
Inferred
|
Explain
|
|
|
91
|
mitochondrial pyruvate dehydrogenase complex
|
Component
|
Inferred
|
Explain
|
|
|
92
|
NADH cytochrome B5 reductase deficiency
|
Disease
|
Inferred
|
Explain
|
|
|
93
|
BCAT2 gene
|
Gene
|
Inferred
|
Explain
|
|
|
94
|
plastid pyruvate dehydrogenase complex
|
Component
|
Inferred
|
Explain
|
|
|
95
|
Dihydrolipoamide acetyltransferase, long form
|
Domain
|
Inferred
|
Explain
|
|
|
96
|
Cyclosporine
|
Compound
|
Known
|
Explain
|
|
|
97
|
Dihydrolipoamide acetyltransferase pyruvate dehydrogenase complex
|
Domain
|
Inferred
|
Explain
|
|
|
98
|
PDK2 gene
|
Gene
|
Inferred
|
Explain
|
|
|
99
|
SHMT1 gene
|
Gene
|
Inferred
|
Explain
|
|
|
100
|
ACR gene
|
Gene
|
Inferred
|
Explain
|
|