Sensorineural Hearing Loss (disorder)

Disease • C0018784

Definition

Hearing loss resulting from damage to the COCHLEA and the sensorineural elements which lie internally beyond the oval and round windows. These elements include the AUDITORY NERVE and its connections in the BRAINSTEM.

Synonyms

Sensorineural Hearing Loss (disorder) • Sensorineural deafness • Deafness, sensorineural • Deafness Sensorineural • Sensorineural deafness NOS • Hearing Loss, Sensorineural • Sensorineural hearing loss • HEARING DISORDER, SENSORINEURAL • DEAFNESS, PERCEPTIVE • HEARING DISORDER, NEURAL • HEARING DISORDER RETROCOCHLEAR • Hearing loss, perceptive • Perceptive hearing loss NOS • Unspecified sensorineural hearing loss • Sensorineural hearing loss, unspecified • Deafness, neurosensory • Perceptive hearing loss or deafness • Sensorneur hear loss NOS • Hearing Loss, Sensorineural [Disease/Finding]

Linked items?Related concepts, ordered by their global importance in the network.

Cisplatin    LRP2 gene    FADD gene    FGF3 gene    GJB2 gene    SLC26A4 gene    Muscular Dystrophy, Facioscapulohumeral    hearing impairment    GJB3 gene    Paraganglioma    Donnai Barrow syndrome    SLC26A5 gene    Gonadal dysgenesis XX type deafness    Barakat syndrome    Progressive hearing loss stapes fixation    Usher Syndrome    NEUROENDOCRINE CARCINOMA OF SALIVARY GLANDS, SENSORINEURAL HEARING LOSS, AND ENAMEL HYPOPLASIA    ALBINISM, OCULAR, WITH LATE-ONSET SENSORINEURAL DEAFNESS (disorder)    ALBINISM, OCULAR, WITH SENSORINEURAL DEAFNESS    BARTTER SYNDROME, TYPE 4A   

Related concepts

# Concept name Type Relation Support Score
1 Noise-induced hearing loss Other Known Explain 2.07659
2 CUTIS VERTICIS GYRATA, RETINITIS PIGMENTOSA, AND SENSORINEURAL DEAFNESS Disease Known Explain 2.01879
3 ROD-CONE DYSTROPHY, SENSORINEURAL DEAFNESS, AND FANCONI-TYPE RENAL DYSFUNCTION Disease Known Explain 1.96152
4 Cleft palate, midfacial hypoplasia, triangular facies, and sensorineural hearing loss Disease Known Explain 1.93785
5 Histiocytosis with joint contractures and sensorineural deafness Disease Known Explain 1.92783
6 CEREBELLAR ATAXIA AND NEUROSENSORY DEAFNESS Disease Known Explain 1.87612
7 SPONDYLOEPIPHYSEAL DYSPLASIA, MYOPIA, AND SENSORINEURAL DEAFNESS Disease Known Explain 1.85140
8 Arthrogryposis-like hand anomaly and sensorineural deafness Disease Known Explain 1.78296
9 Hearing Loss, Central Disease Known Explain 1.75653
10 CARDIOMYOPATHY, DILATED, 1J Disease Known Explain 1.71969
11 Knuckle pads, leuconychia and sensorineural deafness Disease Known Explain 1.71416
12 CAPOS syndrome Disease Known Explain 1.65054
13 ALBINISM, OCULAR, WITH SENSORINEURAL DEAFNESS Disease Known Explain 1.63725
14 FRIEDREICH ATAXIA, SO-CALLED, WITH OPTIC ATROPHY AND SENSORINEURAL DEAFNESS Disease Known Explain 1.62450
15 Fountain syndrome Disease Known Explain 1.56531
16 SPASTIC PARAPLEGIA, SENSORINEURAL DEAFNESS, MENTAL RETARDATION, AND PROGRESSIVE NEPHROPATHY Disease Known Explain 1.56286
17 CORNEAL DYSTROPHY AND PERCEPTIVE DEAFNESS Disease Known Explain 1.55819
18 AXENFELD-RIEGER ANOMALY WITH PARTIALLY ABSENT EYE MUSCLES, DISTINCTIVE FACE, HYDROCEPHALY, AND SKELETAL ABNORMALITIES Disease Known Explain 1.55798
19 CATARACTS, CONGENITAL, WITH SENSORINEURAL DEAFNESS, DOWN SYNDROME-LIKE FACIAL APPEARANCE, SHORT STATURE, AND MENTAL RETARDATION Disease Known Explain 1.54271
20 ALBINISM, OCULAR, WITH LATE-ONSET SENSORINEURAL DEAFNESS (disorder) Disease Known Explain 1.47785
21 BARTTER SYNDROME, TYPE 4A Disease Known Explain 1.47185
22 INSULIN-LIKE GROWTH FACTOR I DEFICIENCY Disease Known Explain 1.46634
23 Nance Sweeney chondrodysplasia Disease Known Explain 1.43989
24 Thiamine responsive megaloblastic anemia syndrome Other Known Explain 1.39731
25 Brown-Vialetto-Van Laere syndrome Disease Known Explain 1.36749
26 Jones syndrome Disease Known Explain 1.36144
27 Usher Syndrome Disease Known Explain 1.31784
28 SPLIT-HAND/FOOT MALFORMATION WITH SENSORINEURAL HEARING LOSS Disease Known Explain 1.30653
29 Progressive hearing loss stapes fixation Disease Known Explain 1.29360
30 NEUROENDOCRINE CARCINOMA OF SALIVARY GLANDS, SENSORINEURAL HEARING LOSS, AND ENAMEL HYPOPLASIA Disease Known Explain 1.24820
31 CORNEAL HYPESTHESIA WITH RETINAL ABNORMALITIES, SENSORINEURAL DEAFNESS, UNUSUAL FACIES, PERSISTENT DUCTUS ARTERIOSUS, AND MENTAL RETARDATION Disease Known Explain 1.24264
32 SLC26A5 gene Gene Known Explain 1.17119
33 Gonadal dysgenesis XX type deafness Other Known Explain 1.07276
34 Barakat syndrome Disease Known Explain 1.01640
35 Donnai Barrow syndrome Disease Known Explain 0.96525
36 GJB2 gene Gene Known Explain 0.80706
37 Paraganglioma Disease Known Explain 0.67906
38 GJB3 gene Gene Known Explain 0.65029
39 Muscular Dystrophy, Facioscapulohumeral Disease Known Explain 0.57324
40 hearing impairment Disease Known Explain 0.54383
41 SLC26A4 gene Gene Known Explain 0.52014
42 Cutis verticis gyrata Disease Inferred Explain 0.48265
43 FGF3 gene Gene Known Explain 0.45508
44 Auditory Diseases, Central Disease Inferred Explain 0.41176
45 Albinism, Ocular Other Inferred Explain 0.40348
46 Joint contracture Other Inferred Explain 0.37868
47 Mental Retardation Disease Inferred Explain 0.32973
48 KNUCKLE PADS Other Inferred Explain 0.30024
49 Cerebellar Ataxia Disease Inferred Explain 0.29744
50 Coarse face Disease Inferred Explain 0.29647
51 Optic Atrophy Disease Inferred Explain 0.25385
52 LRP2 gene Gene Known Explain 0.23303
53 Complete Hearing Loss Disease Inferred Explain 0.22963
54 Myopia Disease Inferred Explain 0.21988
55 Deafness Disease Inferred Explain 0.21731
56 FADD gene Gene Known Explain 0.21654
57 Retinitis Pigmentosa Disease Inferred Explain 0.21210
58 Motor retardation Disease Inferred Explain 0.21131
59 Albinism Other Inferred Explain 0.20568
60 Friedreich Ataxia Disease Inferred Explain 0.19173
61 Orbital separation excessive Other Inferred Explain 0.19060
62 Histiocytosis Disease Inferred Explain 0.17879
63 Bulbar Palsy, Progressive Disease Inferred Explain 0.16677
64 RETINAL ABNORMALITY Disease Inferred Explain 0.15224
65 Fibromatosis, Gingival Other Inferred Explain 0.14753
66 CHONDRODYSTROPHY Disease Inferred Explain 0.14297
67 EYA4 gene Gene Inferred Explain 0.12477
68 Arthrogryposis Other Inferred Explain 0.12467
69 Stapes fixation Other Inferred Explain 0.11044
70 Carcinoma, Neuroendocrine Disease Inferred Explain 0.10699
71 MENTAL RETARDATION, MICROCEPHALY, GROWTH RETARDATION, JOINT CONTRACTURES, AND FACIAL DYSMORPHISM Disease Inferred Explain 0.10517
72 Patent ductus arteriosus Other Inferred Explain 0.09707
73 CLCNKA gene Gene Inferred Explain 0.08883
74 Anemia, Megaloblastic Disease Inferred Explain 0.08763
75 Cleft Palate Other Inferred Explain 0.08489
76 CUTIS VERTICIS GYRATA, THYROID APLASIA, AND MENTAL RETARDATION Disease Inferred Explain 0.08304
77 CUTIS VERTICIS GYRATA AND MENTAL DEFICIENCY Disease Inferred Explain 0.08304
78 Fibromatosis Disease Inferred Explain 0.07987
79 Salivary Gland Diseases Disease Inferred Explain 0.07864
80 Gingiva Other Inferred Explain 0.07845
81 Growth retardation Disease Inferred Explain 0.07761
82 Salivary Glands Other Inferred Explain 0.07688
83 CLCNKB gene Gene Inferred Explain 0.07381
84 Dental Enamel Hypoplasia Disease Inferred Explain 0.06996
85 BSND gene Gene Inferred Explain 0.06981
86 Bartter Disease Disease Inferred Explain 0.05767
87 Deaf-Blind Disorders Disease Inferred Explain 0.05728
88 Ovarian dysgenesis Other Inferred Explain 0.05684
89 Cisplatin Compound Known Explain 0.05642
90 COL11A2 gene Gene Inferred Explain 0.05609
91 C1848408 Other Inferred Explain 0.05496
92 Spastic Paraplegia Disease Inferred Explain 0.05319
93 Short stature Disease Inferred Explain 0.05129
94 SLC19A2 gene Gene Inferred Explain 0.04940
95 Ovarian failure Disease Inferred Explain 0.04796
96 Hydrocephalus Disease Inferred Explain 0.04477
97 Aniridia renal agenesis psychomotor retardation Disease Inferred Explain 0.04134
98 POU3F4 gene Gene Inferred Explain 0.04010
99 Congenital exomphalos Other Inferred Explain 0.03963
100 Foot Other Inferred Explain 0.03928