Factor X Deficiency

Disease • C0015519

Definition

Blood coagulation disorder usually inherited as an autosomal recessive trait, though it can be acquired. It is characterized by defective activity in both the intrinsic and extrinsic pathways, impaired thromboplastin time, and impaired prothrombin consump

Synonyms

Factor X Deficiency • Deficiency, factor X • Deficiencies, Factor X • Factor X Deficiencies • Stuart-Prower Deficiency • Stuart Prower Deficiency • Deficiency, Stuart Prower • Deficiency, Stuart-Prower • Stuart-Prower Factor Deficiency • Stuart Prower Factor Deficiency • Deficiency, Stuart Prower Factor • Deficiency, Stuart-Prower Factor • Disease, Stuart-Prower • DEFIC FACTOR X • FACTOR X DEFIC • DEFIC STUART PROWER • STUART PROWER DEFIC • DEFIC STUART PROWER FACTOR • STUART PROWER FACTOR DEFIC • Factor X Deficiency [Disease/Finding]

Linked items?Related concepts, ordered by their global importance in the network.

F10 gene    Hemorrhagic Disorders    Blood Coagulation Disorders, Inherited    Coagulation Protein Disorders   

Related concepts

# Concept name Type Relation Support Score
1 Coagulation Protein Disorders Disease Known Explain 118.25861
2 Blood Coagulation Disorders, Inherited Disease Known Explain 88.39596
3 Hemorrhagic Disorders Disease Known Explain 80.17890
4 F10 gene Gene Known Explain 36.00591
5 Factor VII Deficiency Disease Inferred Explain 3.52865
6 Hypoprothrombinemias Disease Inferred Explain 3.52146
7 Factor V Deficiency Disease Inferred Explain 3.52115
8 Factor XI Deficiency Disease Inferred Explain 3.46415
9 Factor XII Deficiency Disease Inferred Explain 3.41188
10 Factor XIII Deficiency Disease Inferred Explain 3.24389
11 Hemophilia B Disease Inferred Explain 3.12802
12 Afibrinogenemia Disease Inferred Explain 3.11112
13 Hemophilia A Disease Inferred Explain 2.76425
14 von Willebrand Disease Disease Inferred Explain 2.40091
15 Activated Protein C Resistance Disease Inferred Explain 2.19963
16 Blood Coagulation Disorders Disease Inferred Explain 1.33081
17 Thrombasthenia Disease Inferred Explain 1.01938
18 Wiskott-Aldrich Syndrome Disease Inferred Explain 0.93069
19 Hermanski-Pudlak Syndrome Disease Inferred Explain 0.86944
20 Bernard-Soulier Syndrome Disease Inferred Explain 0.80703
21 Blood Platelet Disorders Disease Inferred Explain 0.66410
22 Platelet Storage Pool Deficiency Disease Inferred Explain 0.50655
23 Gray Platelet Syndrome Disease Inferred Explain 0.43070
24 Disseminated Intravascular Coagulation Disease Inferred Explain 0.40515
25 F7 gene Gene Inferred Explain 0.40230
26 Thrombophilia Disease Inferred Explain 0.36330
27 Antithrombin III Deficiency Disease Inferred Explain 0.35352
28 Thrombocythemia, Essential Disease Inferred Explain 0.34499
29 Protein C Deficiency Disease Inferred Explain 0.33352
30 Vitamin K Deficiency Disease Inferred Explain 0.32734
31 Waterhouse-Friderichsen Syndrome Disease Inferred Explain 0.25221
32 F9 gene Gene Inferred Explain 0.22759
33 Purpura, Thrombocytopenic, Idiopathic Disease Inferred Explain 0.22013
34 F5 gene Gene Inferred Explain 0.21458
35 F13B gene Gene Inferred Explain 0.19203
36 F11 gene Gene Inferred Explain 0.18402
37 Hereditary factor I deficiency disease Disease Inferred Explain 0.18219
38 Hematological Disease Disease Inferred Explain 0.16301
39 Genetic Diseases, X-Linked Disease Inferred Explain 0.13007
40 Vascular Hemostatic Disorders Disease Inferred Explain 0.11795
41 F12 gene Gene Inferred Explain 0.10946
42 Embolism and Thrombosis Disease Inferred Explain 0.10775
43 FGA gene Gene Inferred Explain 0.10488
44 FGB gene Gene Inferred Explain 0.09906
45 F13A1 gene Gene Inferred Explain 0.09691
46 F2 gene Gene Inferred Explain 0.08521
47 CFI gene Gene Inferred Explain 0.08137
48 PROC gene Gene Inferred Explain 0.07649
49 P2RX1 gene Gene Inferred Explain 0.06204
50 Lymphopenia Disease Inferred Explain 0.05890
51 Blood Protein Disorders Disease Inferred Explain 0.05861
52 F8 gene Gene Inferred Explain 0.04718
53 Genetic Diseases, Inborn Disease Inferred Explain 0.04542
54 Malnutrition Disease Inferred Explain 0.04441
55 MTHFR gene Gene Inferred Explain 0.04125
56 GIANT PLATELET SYNDROME WITH THROMBOCYTOPENIA Disease Inferred Explain 0.04091
57 HEMOPHILIA A WITH VASCULAR ABNORMALITY Disease Inferred Explain 0.03999
58 Protein S Deficiency Disease Inferred Explain 0.03991
59 VWF gene Gene Inferred Explain 0.03873
60 2-(4-((1-acetimidoyl-3-pyrrolidinyl)oxy)phenyl)-3-(7-amidino-2-naphthyl)propanoic acid hydrocloride pentahydrate Compound Inferred Explain 0.03632
61 fondaparinux Compound Inferred Explain 0.03632
62 idraparinux Compound Inferred Explain 0.03632
63 1-(3'-aminobenzisoxazol-5'-yl)-3-trifluoromethyl-N-(2-fluoro-4-((2'-dimethylaminomethyl)imidazol-1-yl)phenyl)-1H-pyrazole-5-carboxamide Compound Inferred Explain 0.03632
64 BAY 59-7939 Compound Inferred Explain 0.03632
65 GGCX gene Gene Inferred Explain 0.03613
66 Thrombocytosis Disease Inferred Explain 0.03594
67 blood coagulation, extrinsic pathway Function Inferred Explain 0.03468
68 Gestodene Compound Inferred Explain 0.03347
69 EPR1 gene Gene Inferred Explain 0.03329
70 CycloProvera Compound Inferred Explain 0.03261
71 Mesigyna Compound Inferred Explain 0.03261
72 Purpura Disease Inferred Explain 0.03151
73 Blood Platelets Other Inferred Explain 0.03035
74 blood coagulation, intrinsic pathway Function Inferred Explain 0.03026
75 von Willebrand Disease, Type 3 Disease Inferred Explain 0.02968
76 VON WILLEBRAND DISEASE, X-LINKED FORM Disease Inferred Explain 0.02968
77 GP1BA gene Gene Inferred Explain 0.02948
78 GP9 gene Gene Inferred Explain 0.02908
79 Von Willebrand disease, platelet type Disease Inferred Explain 0.02908
80 von Willebrand Disease, Recessive Form Disease Inferred Explain 0.02835
81 Immunologic Deficiency Syndromes Disease Inferred Explain 0.02564
82 peptidyl-glutamic acid carboxylation Function Inferred Explain 0.02468
83 GP1BB gene Gene Inferred Explain 0.02312
84 SERPINC1 gene Gene Inferred Explain 0.01913
85 Warfarin Compound Inferred Explain 0.01889
86 Complement and coagulation cascades - Homo sapiens (human) Pathway Inferred Explain 0.01869
87 Norethindrone Compound Inferred Explain 0.01843
88 ITGA2B gene Gene Inferred Explain 0.01832
89 PROS1 gene Gene Inferred Explain 0.01811
90 propylene dichloride Compound Inferred Explain 0.01705
91 SERPINA10 gene Gene Inferred Explain 0.01691
92 intrinsic to external side of plasma membrane Component Inferred Explain 0.01612
93 Thrombocytopenia Disease Inferred Explain 0.01566
94 Golgi lumen Component Inferred Explain 0.01554
95 SERPINB6 gene Gene Inferred Explain 0.01340
96 Ethionine Compound Inferred Explain 0.01334
97 SERPINA5 gene Gene Inferred Explain 0.01242
98 SERPINB8 gene Gene Inferred Explain 0.01175
99 TFPI gene Gene Inferred Explain 0.01144
100 Ecchymosis Disease Inferred Explain 0.01142