Factor V Deficiency

Disease • C0015499

Definition

A deficiency of blood coagulation factor V (known as proaccelerin or accelerator globulin or labile factor) leading to a rare hemorrhagic tendency known as Owren's disease or parahemophilia. It varies greatly in severity. Factor V deficiency is an autosom

Synonyms

Factor V Deficiency • Deficiency, factor V • Deficiencies, Factor V • Factor V Deficiencies • ACCELERATOR GLOBULIN DEFICIENCY • FACTOR V DEFICIENCY, CONGENITAL • LABILE FACTOR DEFICIENCY • PROACCELERIN DEFICIENCY • Deficiency, proaccelerin • Owren Disease • Disease, Owren's • Owren's disease • Diseases, Owren • Diseases, Owren's • Owren Diseases • Owren's Diseases • Owrens Disease • Disease, Owren • Parahemophilia • AC globulin deficiency • Deficiency, AC globulin • Parahemophilias • Deficiency, labile • DEFIC FACTOR V • FACTOR V DEFIC • OWREN PARAHEMOPHILIA • Factor V Deficiency [Disease/Finding]

Linked items?Related concepts, ordered by their global importance in the network.

F5 gene    Hemorrhagic Disorders    Blood Coagulation Disorders, Inherited    Coagulation Protein Disorders   

Related concepts

# Concept name Type Relation Support Score
1 Coagulation Protein Disorders Disease Known Explain 118.23748
2 Blood Coagulation Disorders, Inherited Disease Known Explain 88.38371
3 Hemorrhagic Disorders Disease Known Explain 80.13242
4 F5 gene Gene Known Explain 44.66970
5 Hypoprothrombinemias Disease Inferred Explain 3.51728
6 Factor VII Deficiency Disease Inferred Explain 3.51365
7 Factor X Deficiency Disease Inferred Explain 3.48088
8 Factor XI Deficiency Disease Inferred Explain 3.45626
9 Factor XII Deficiency Disease Inferred Explain 3.40567
10 Factor XIII Deficiency Disease Inferred Explain 3.23918
11 Hemophilia B Disease Inferred Explain 3.11600
12 Afibrinogenemia Disease Inferred Explain 3.10539
13 Hemophilia A Disease Inferred Explain 2.73923
14 von Willebrand Disease Disease Inferred Explain 2.39649
15 Activated Protein C Resistance Disease Inferred Explain 2.19923
16 Blood Coagulation Disorders Disease Inferred Explain 1.52851
17 Thrombasthenia Disease Inferred Explain 1.01828
18 Wiskott-Aldrich Syndrome Disease Inferred Explain 0.92905
19 Hermanski-Pudlak Syndrome Disease Inferred Explain 0.87135
20 Bernard-Soulier Syndrome Disease Inferred Explain 0.80472
21 Blood Platelet Disorders Disease Inferred Explain 0.66616
22 Platelet Storage Pool Deficiency Disease Inferred Explain 0.51666
23 Gray Platelet Syndrome Disease Inferred Explain 0.43027
24 Disseminated Intravascular Coagulation Disease Inferred Explain 0.41531
25 Thrombophilia Disease Inferred Explain 0.36996
26 Antithrombin III Deficiency Disease Inferred Explain 0.35398
27 Thrombocythemia, Essential Disease Inferred Explain 0.35328
28 Protein C Deficiency Disease Inferred Explain 0.33934
29 Vitamin K Deficiency Disease Inferred Explain 0.33515
30 F7 gene Gene Inferred Explain 0.26442
31 Waterhouse-Friderichsen Syndrome Disease Inferred Explain 0.25253
32 Purpura, Thrombocytopenic, Idiopathic Disease Inferred Explain 0.21980
33 F13B gene Gene Inferred Explain 0.19159
34 F9 gene Gene Inferred Explain 0.18717
35 Hereditary factor I deficiency disease Disease Inferred Explain 0.18168
36 F11 gene Gene Inferred Explain 0.17545
37 Hematological Disease Disease Inferred Explain 0.16673
38 F10 gene Gene Inferred Explain 0.16267
39 Genetic Diseases, X-Linked Disease Inferred Explain 0.12962
40 Vascular Hemostatic Disorders Disease Inferred Explain 0.11831
41 F12 gene Gene Inferred Explain 0.10479
42 FGA gene Gene Inferred Explain 0.10371
43 F2 gene Gene Inferred Explain 0.10029
44 F13A1 gene Gene Inferred Explain 0.09805
45 FGB gene Gene Inferred Explain 0.09595
46 CFI gene Gene Inferred Explain 0.08095
47 PROC gene Gene Inferred Explain 0.07957
48 P2RX1 gene Gene Inferred Explain 0.06199
49 Blood Protein Disorders Disease Inferred Explain 0.06038
50 Lymphopenia Disease Inferred Explain 0.05878
51 Venous Thrombosis Disease Inferred Explain 0.04803
52 Genetic Diseases, Inborn Disease Inferred Explain 0.04540
53 Malnutrition Disease Inferred Explain 0.04435
54 Protein S Deficiency Disease Inferred Explain 0.04368
55 Warfarin Compound Inferred Explain 0.04272
56 MTHFR gene Gene Inferred Explain 0.04251
57 Budd-Chiari Syndrome Disease Inferred Explain 0.04221
58 EPR1 gene Gene Inferred Explain 0.04209
59 Hepatic Vein Thrombosis Disease Inferred Explain 0.04140
60 GIANT PLATELET SYNDROME WITH THROMBOCYTOPENIA Disease Inferred Explain 0.04071
61 HEMOPHILIA A WITH VASCULAR ABNORMALITY Disease Inferred Explain 0.03800
62 VWF gene Gene Inferred Explain 0.03705
63 Thrombocytosis Disease Inferred Explain 0.03638
64 Purpura Disease Inferred Explain 0.03393
65 Mercilon Compound Inferred Explain 0.03292
66 Retinal Vein Occlusion Disease Inferred Explain 0.03289
67 Blood Platelets Other Inferred Explain 0.03028
68 von Willebrand Disease, Type 3 Disease Inferred Explain 0.02958
69 VON WILLEBRAND DISEASE, X-LINKED FORM Disease Inferred Explain 0.02958
70 Von Willebrand disease, platelet type Disease Inferred Explain 0.02894
71 von Willebrand Disease, Recessive Form Disease Inferred Explain 0.02823
72 GP1BA gene Gene Inferred Explain 0.02811
73 Ischemic stroke Disease Inferred Explain 0.02765
74 GP9 gene Gene Inferred Explain 0.02655
75 F8 gene Gene Inferred Explain 0.02564
76 Immunologic Deficiency Syndromes Disease Inferred Explain 0.02562
77 Clomiphene Compound Inferred Explain 0.02469
78 GP1BB gene Gene Inferred Explain 0.02112
79 MMRN1 gene Gene Inferred Explain 0.01871
80 ITGA2B gene Gene Inferred Explain 0.01871
81 Complement and coagulation cascades - Homo sapiens (human) Pathway Inferred Explain 0.01851
82 propylene dichloride Compound Inferred Explain 0.01847
83 PROS1 gene Gene Inferred Explain 0.01835
84 Levonorgestrel Compound Inferred Explain 0.01674
85 Ethionine Compound Inferred Explain 0.01552
86 Thrombocytopenia Disease Inferred Explain 0.01460
87 platelet alpha granule lumen Component Inferred Explain 0.01355
88 Ecchymosis Disease Inferred Explain 0.01333
89 GGCX gene Gene Inferred Explain 0.01245
90 Benzbromarone Compound Inferred Explain 0.01225
91 Propylthiouracil Compound Inferred Explain 0.01173
92 Avitaminosis Disease Inferred Explain 0.01070
93 Thrombocytopenic purpura Disease Inferred Explain 0.01023
94 WAS gene Gene Inferred Explain 0.01006
95 Vitamin K Deficiency Bleeding Disease Inferred Explain 0.00975
96 ITGB3 gene Gene Inferred Explain 0.00970
97 platelet degranulation Function Inferred Explain 0.00968
98 Clofibrate Compound Inferred Explain 0.00926
99 SERPINC1 gene Gene Inferred Explain 0.00898
100 CTSG gene Gene Inferred Explain 0.00892