Deafness

Disease • C0011053

Definition

A partial or complete loss o f hearing in one or both ears; the level of impairment varies from a mild but important loss of sensitivity to a total loss of hearing.

Synonyms

Deafness • DEAFNESS (NOS) • Deafness NOS • Deafness all degrees NOS

Linked items?Related concepts, ordered by their global importance in the network.

Wolfram Syndrome    Gonadal dysgenesis XX type deafness    DISLOCATED ELBOWS, BOWED TIBIAS, SCOLIOSIS, DEAFNESS, CATARACT, MICROCEPHALY, AND MENTAL RETARDATION    Townes syndrome    RETINITIS PIGMENTOSA, DEAFNESS, MENTAL RETARDATION, AND HYPOGONADISM    Dementia, familial Danish    CHARCOT-MARIE-TOOTH DISEASE, X-LINKED RECESSIVE, 5    ATHEROSCLEROSIS, PREMATURE, WITH DEAFNESS, NEPHROPATHY, DIABETES MELLITUS, PHOTOMYOCLONUS, AND DEGENERATIVE NEUROLOGIC DISEASE    Jervell-Lange Nielsen Syndrome    COWCHOCK SYNDROME    Progressive hearing loss stapes fixation    Juberg-Marsidi syndrome    ATAXIA, FATAL X-LINKED, WITH DEAFNESS AND LOSS OF VISION    OPTIC ATROPHY 1 AND DEAFNESS    Alport Syndrome, X-Linked    Fechtner syndrome (disorder)    Nephrosis deafness urinary tract digital malformation    DEAFNESS, AUTOSOMAL RECESSIVE 31    EPIPHYSEAL DYSPLASIA OF FEMORAL HEAD, MYOPIA, AND DEAFNESS    DEAFNESS, CONGENITAL, WITH VITILIGO AND ACHALASIA   

Related concepts

# Concept name Type Relation Support Score
1 Complete Hearing Loss Disease Inferred Explain 23.90724
2 DEAFNESS, PROGRESSIVE, WITH STAPES FIXATION Disease Known Explain 0.28641
3 Stoll Levy Francfort syndrome Disease Known Explain 0.25906
4 DEAFNESS, AUTOSOMAL RECESSIVE 9 Disease Known Explain 0.25741
5 DEAFNESS, PROGRESSIVE HIGH-TONE NEURAL Disease Known Explain 0.25445
6 C1832186 Other Known Explain 0.25445
7 DEAFNESS, AUTOSOMAL DOMINANT 7 (disorder) Disease Known Explain 0.25445
8 DEAFNESS, AUTOSOMAL RECESSIVE 5 (disorder) Disease Known Explain 0.25445
9 DEAFNESS, AUTOSOMAL RECESSIVE 68 Disease Known Explain 0.25445
10 DEAFNESS, AUTOSOMAL RECESSIVE 48 Disease Known Explain 0.25445
11 DEAFNESS, AUTOSOMAL RECESSIVE 32 Disease Known Explain 0.25445
12 DEAFNESS, AUTOSOMAL DOMINANT 47 (disorder) Disease Known Explain 0.25445
13 DEAFNESS, AUTOSOMAL DOMINANT 31 (disorder) Disease Known Explain 0.25445
14 C1838649 Other Known Explain 0.25445
15 DEAFNESS, AUTOSOMAL DOMINANT 43 (disorder) Disease Known Explain 0.25445
16 DEAFNESS, AUTOSOMAL DOMINANT 49 (disorder) Disease Known Explain 0.25445
17 DEAFNESS, AUTOSOMAL RECESSIVE 40 (disorder) Disease Known Explain 0.25445
18 DEAFNESS, AUTOSOMAL DOMINANT 41 (disorder) Disease Known Explain 0.25445
19 DEAFNESS, AUTOSOMAL RECESSIVE 38 Disease Known Explain 0.25445
20 C1842938 Other Known Explain 0.25445
21 DEAFNESS, AUTOSOMAL DOMINANT 52 Disease Known Explain 0.25445
22 DEAFNESS, AUTOSOMAL RECESSIVE 33 Disease Known Explain 0.25445
23 DEAFNESS, AUTOSOMAL RECESSIVE (disorder) Disease Known Explain 0.25445
24 DEAFNESS, AUTOSOMAL DOMINANT 21 (disorder) Disease Known Explain 0.25445
25 DEAFNESS, AUTOSOMAL DOMINANT 30 (disorder) Disease Known Explain 0.25445
26 RETINITIS PIGMENTOSA INVERSA WITH DEAFNESS Disease Known Explain 0.25445
27 DEAFNESS WITH ANHIDROTIC ECTODERMAL DYSPLASIA Disease Known Explain 0.25445
28 DEAFNESS, MID-TONE NEURAL Disease Known Explain 0.25445
29 DEAFNESS, AUTOSOMAL RECESSIVE 65 Disease Known Explain 0.25445
30 DEAFNESS, AUTOSOMAL DOMINANT 24 (disorder) Disease Known Explain 0.25445
31 DEAFNESS, AUTOSOMAL DOMINANT 18 (disorder) Disease Known Explain 0.25445
32 DEAFNESS, AUTOSOMAL RECESSIVE 27 Disease Known Explain 0.25445
33 DEAFNESS, AUTOSOMAL RECESSIVE 26 Disease Known Explain 0.25445
34 C1857331 Other Known Explain 0.25445
35 DEAFNESS, NEURAL, WITH ATYPICAL ATOPIC DERMATITIS Disease Known Explain 0.25445
36 DEAFNESS, NEURAL, CONGENITAL MODERATE Disease Known Explain 0.25445
37 DEAFNESS, CONDUCTIVE, WITH MALFORMED EXTERNAL EAR Disease Known Explain 0.25445
38 DEAFNESS, CONGENITAL, AND FAMILIAL MYOCLONIC EPILEPSY Disease Known Explain 0.25445
39 C1857349 Other Known Explain 0.25445
40 DEAFNESS, AUTOSOMAL RECESSIVE 66 Disease Known Explain 0.25445
41 DEAFNESS, AUTOSOMAL RECESSIVE 44 Disease Known Explain 0.25445
42 DEAFNESS, AUTOSOMAL RECESSIVE 62 Disease Known Explain 0.25445
43 DEAFNESS, AUTOSOMAL RECESSIVE 20 Disease Known Explain 0.25445
44 DEAFNESS, AUTOSOMAL DOMINANT 16 Disease Known Explain 0.25445
45 DEAFNESS, AUTOSOMAL RECESSIVE 14 Disease Known Explain 0.25445
46 DEAFNESS, AUTOSOMAL RECESSIVE 13 Disease Known Explain 0.25445
47 DEAFNESS, AUTOSOMAL RECESSIVE 17 (disorder) Disease Known Explain 0.25445
48 DEAFNESS, AUTOSOMAL RECESSIVE 46 (disorder) Disease Known Explain 0.25445
49 DEAFNESS, AUTOSOMAL DOMINANT 53 (disorder) Disease Known Explain 0.25445
50 DEAFNESS, AUTOSOMAL RECESSIVE 55 Disease Known Explain 0.25445
51 DEAFNESS, AUTOSOMAL RECESSIVE 47 (disorder) Disease Known Explain 0.25445
52 DEAFNESS, AUTOSOMAL RECESSIVE 51 Disease Known Explain 0.25445
53 SPONDYLOMEGAEPIPHYSEAL DYSPLASIA WITH UPPER LIMB MESOMELIA, PUNCTATE CALCIFICATIONS, AND DEAFNESS Disease Known Explain 0.25445
54 DEAFNESS, AUTOSOMAL RECESSIVE 15 Disease Known Explain 0.25445
55 DEAFNESS, CONDUCTIVE STAPEDIAL, WITH EAR MALFORMATION AND FACIAL PALSY Disease Known Explain 0.24734
56 DEAFNESS, AUTOSOMAL RECESSIVE 7 Disease Known Explain 0.24476
57 DEAFNESS, AUTOSOMAL DOMINANT 36 Disease Known Explain 0.24476
58 DEAFNESS, ONYCHODYSTROPHY, OSTEODYSTROPHY, AND MENTAL RETARDATION SYNDROME Disease Known Explain 0.24368
59 C1969954 Other Known Explain 0.24368
60 DEAFNESS, AUTOSOMAL RECESSIVE, 24 Disease Known Explain 0.24319
61 DEAFNESS, SENSORINEURAL, AND MALE INFERTILITY Disease Known Explain 0.23977
62 DEAFNESS, AUTOSOMAL RECESSIVE 28 Disease Known Explain 0.23967
63 DEAFNESS, SENSORINEURAL, WITH PERIPHERAL NEUROPATHY AND ARTERIAL DISEASE Disease Known Explain 0.23959
64 DEAFNESS, AUTOSOMAL DOMINANT 44 Disease Known Explain 0.23937
65 DEAFNESS, AUTOSOMAL RECESSIVE 39 (disorder) Disease Known Explain 0.23764
66 DEAFNESS, AUTOSOMAL RECESSIVE 37 Disease Known Explain 0.23737
67 DEAFNESS, AUTOSOMAL DOMINANT 20 Disease Known Explain 0.23728
68 Arthrogryposis multiplex with deafness, inguinal hernias, and early death Disease Known Explain 0.23723
69 DEAFNESS, CHILDHOOD-ONSET NEUROSENSORY, AUTOSOMAL RECESSIVE 8 Disease Known Explain 0.23718
70 DEAFNESS, AUTOSOMAL RECESSIVE 10 Disease Known Explain 0.23718
71 DEAFNESS, AUTOSOMAL DOMINANT 4 Disease Known Explain 0.23712
72 DEAFNESS, AUTOSOMAL DOMINANT 15 Disease Known Explain 0.23672
73 DEAFNESS, AUTOSOMAL RECESSIVE 16 Disease Known Explain 0.23574
74 DEAFNESS, AUTOSOMAL RECESSIVE 30 Disease Known Explain 0.23565
75 DEAFNESS, AUTOSOMAL DOMINANT 11 Disease Known Explain 0.23561
76 DEAFNESS, AUTOSOMAL RECESSIVE 2 Disease Known Explain 0.23561
77 DEAFNESS, AUTOSOMAL DOMINANT 17 Disease Known Explain 0.23552
78 DEAFNESS, AUTOSOMAL RECESSIVE 49 Disease Known Explain 0.23512
79 DEAFNESS, AUTOSOMAL RECESSIVE 23 Disease Known Explain 0.23488
80 DEAFNESS, AUTOSOMAL DOMINANT 23 Disease Known Explain 0.23486
81 DEAFNESS, AUTOSOMAL RECESSIVE 22 Disease Known Explain 0.23473
82 DEAFNESS, AUTOSOMAL DOMINANT 10 Disease Known Explain 0.23471
83 DEAFNESS, AUTOSOMAL RECESSIVE 42 (disorder) Disease Known Explain 0.23468
84 DEAFNESS, AUTOSOMAL RECESSIVE 59 Disease Known Explain 0.23461
85 WOLFRAM SYNDROME, MITOCHONDRIAL FORM Disease Known Explain 0.23429
86 DEAFNESS, AUTOSOMAL RECESSIVE 36 Disease Known Explain 0.23426
87 DEAFNESS, AUTOSOMAL RECESSIVE 3 Disease Known Explain 0.23419
88 DEAFNESS, AUTOSOMAL DOMINANT 12 Disease Known Explain 0.23413
89 DEAFNESS, AUTOSOMAL RECESSIVE 21 Disease Known Explain 0.23413
90 DEAFNESS, AUTOSOMAL DOMINANT 5 (disorder) Disease Known Explain 0.23407
91 NEPHROPATHY, PROGRESSIVE, WITH DEAFNESS Disease Known Explain 0.23396
92 DEAFNESS, AUTOSOMAL RECESSIVE 35 Disease Known Explain 0.23336
93 DEAFNESS, AUTOSOMAL DOMINANT 1 (disorder) Disease Known Explain 0.23330
94 DEAFNESS, AUTOSOMAL RECESSIVE 6 Disease Known Explain 0.23296
95 DEAFNESS, AUTOSOMAL DOMINANT 28 Disease Known Explain 0.23255
96 Herrmann syndrome Disease Known Explain 0.23242
97 DEAFNESS, AUTOSOMAL DOMINANT 9 Disease Known Explain 0.23233
98 Progressive hearing loss stapes fixation Disease Known Explain 0.23189
99 DEAFNESS, AUTOSOMAL RECESSIVE 53 Disease Known Explain 0.23163
100 DEAFNESS, AUTOSOMAL DOMINANT 13 Disease Known Explain 0.23163